CREUTZFELDT JAKOB TSE PRION DISEASE
HUMANS END OF YEAR REVIEW DECEMBER 25, 2012
Creutzfeldt-Jakob Disease (CJD) |
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Creutzfeldt-Jakob Disease Sporadic and Familial Case Count | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
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Creutzfeldt-Jakob Disease Surveillance Data for Reporting Years 2002-2011 A total of 165 people died from CJD during 2002-2011. Texas has had one variant CJD case in 2006. Investigators have concluded that the patient was a former resident of the United Kingdom where exposure was likely to have occurred. | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
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Texas CJD Cases by Age and Gender 2002-2011 | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
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CJD Cases by County 2000-2010  | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
Last updated August 24,
2012
PLEASE NOTICE THE TWO OUTBREAKS NO ONE SPEAKS OF IN TEXAS, explained away
by geographical boundaries and mathematics there from, which we all know is a
hoax. CJD clusters can happen close to borders, yet, explained away with
population total, even though the cluster was geographically centered. TSE prion
disease know no boundaries or borders, and TSE prion disease know no age groups.
...TSS
Merry Christmas everyone. ...warmest regards, terry
Wednesday, November 9, 2011
sporadic FFI or nvCJD in TEXAS ?
Case report Sporadic fatal insomnia in a young woman: A diagnostic
challenge: Case Report TEXAS
HOW TO TURN A POTENTIAL MAD COW VICTIM IN THE USA, INTO A HAPPENSTANCE OF
BAD LUCK, A SPONTANEOUS MUTATION FROM NOTHING.
OR WAS IT $$$
USA PRION UNIT LATEST HUMAN TSE PRION DISEASE UPDATE AUGUST 14, 2012
National Prion Disease Pathology Surveillance Center Cases Examined1
(August 14, 2012)
1996 & earlier 28 cases of sporadic CJD.
see steady increase to ;
2010 cases of sporadic CJD 216.
2011 cases of sporadic CJD 214.
snip...
1 Listed based on the year of death or, if not available, on year of
referral;
2 Cases with suspected prion disease for which brain tissue and/or blood
(in familial cases) were submitted;
3 Disease acquired in the United Kingdom;
4 Disease was acquired in the United Kingdom in one case and in Saudi
Arabia in the other case;
5 Includes 8 cases in which the diagnosis is pending, and 18 inconclusive
cases;
6 Includes 10 (9 from 2012) cases with type determination pending in which
the diagnosis of vCJD has been excluded.
The Sporadic cases include 16 cases of sporadic Fatal Insomnia (sFI) and 42
cases of Variably Protease-Sensitive Prionopathy (VPSPr) and 2224 cases of
sporadic Creutzfeldt-Jakob disease (sCJD).
snip...see full case reports here ;
Tuesday, December 18, 2012
Bioassay Studies Support the Potential for Iatrogenic Transmission of
Variant Creutzfeldt Jakob Disease through Dental Procedures
Sunday, December 9, 2012
Prions, prionoids and pathogenic proteins in Alzheimer disease
Tuesday, December 04, 2012
Veterans health administration information systems as a resource for rare
disorders research: Creutzfeldt-Jakob disease as a paradigm
Friday, November 23, 2012
sporadic Creutzfeldt-Jakob Disease update As at 5th November 2012 UK, USA,
AND CANADA
snip...
Greetings BSE-L members et al, and others,
Confucius is confused again on the infamous ‘classification pending
sporadic creutzfeldt jakob disease’ cpsCJD, (because nvCJD has been ruled out).
Confucius is confused about why the increase of these cpsCJD cases in the
USA and Canada which we have been seeing, but I saw no reports in the UK
surveillance reports of the infamous North American Classification Pending
Sporadic Creutzfeldt Jakob disease cases.
if truly a supposedly sporadic spontaneous disease, would you not see these
cpsCJD cases popping up all over the world in random ???
or, could these cpsCJD cases be of a North American zoonotic or iatrogenic
from North American zoonoses sub-clinical source ???
or both ???
with so many documented Transmissible Spongiform Encephalopathy TSE prion
disease in so many different species here in North America, and consumption
there from, I believe that this should be at the forefront of research. ...
Confused Confucius...flounder
USA
*** 5 Includes 8 cases in which the diagnosis is pending, and 18
inconclusive cases;
*** 6 Includes 10 (9 from 2012) cases with type determination pending in
which the diagnosis of vCJD has been excluded.
Canada
*** 3. Final classification of 48 cases from 2009, 2010, 2011 and 2012 is
pending.
MEXICO
clueless
AS OF AUGUST 2012 ;
CJD UPDATE USA
1 Listed based on the year of death or, if not available, on year of
referral;
2 Cases with suspected prion disease for which brain tissue and/or blood
(in familial cases) were submitted;
3 Disease acquired in the United Kingdom;
4 Disease was acquired in the United Kingdom in one case and in Saudi
Arabia in the other case;
*** 5 Includes 8 cases in which the diagnosis is pending, and 18
inconclusive cases;
*** 6 Includes 10 (9 from 2012) cases with type determination pending in
which the diagnosis of vCJD has been excluded.
*** The Sporadic cases include 16 cases of sporadic Fatal Insomnia (sFI)
and 42 cases of Variably Protease-Sensitive Prionopathy (VPSPr) and 2224 cases
of sporadic Creutzfeldt-Jakob disease (sCJD).
CJD Deaths Reported by CJDSS1, 1994-20122
As of Oct 31, 2012
Deaths of Definite and Probable CJD
Year Sporadic Iatrogenic Familial GSS FFI vCJD Total
1994 2 0 0 1 0 0 3
1995 3 0 0 0 0 0 3
1996 13 0 0 0 0 0 13
1997 16 0 1 1 0 0 18
1998 22 1 0 1 0 0 24
1999 27 2 2 1 0 0 32
2000 32 0 0 3 0 0 35
2001 27 0 2 1 0 0 30
2002 31 0 2 2 0 1 36
2003 27 1 1 0 0 0 29
2004 42 0 1 1 0 0 44
2005 41 0 1 1 0 0 43
2006 39 0 1 3 1 0 44
2007 35 0 0 4 0 0 39
2008 48 0 1 0 0 0 49
2009 48 0 3 2 0 0 53
2010 35 0 3 0 0 0 38
2011 41 0 2 1 0 1 45
2012 20 0 0 0 0 0 20
Total 549 4 20 22 1 2 598
1. CJDSS began in 1998
2. Data before 1998 are retrospective and partial, data from 1998 to 2008
are complete, and data for 2009 - 2012 are provisional
3. Final classification of 48 cases from 2009, 2010, 2011 and 2012 is
pending.
snip...see full text ;
Tuesday, November 6, 2012
Transmission of New Bovine Prion to Mice, Atypical Scrapie, BSE, and
Sporadic CJD, November-December 2012 update
Saturday, March 5, 2011
MAD COW ATYPICAL CJD PRION TSE CASES WITH CLASSIFICATIONS PENDING ON THE
RISE IN NORTH AMERICA
Tuesday, June 1, 2010
USA cases of dpCJD rising with 24 cases so far in 2010
Monday, April 5, 2010
UPDATE - CJD TEXAS 38 YEAR OLD FEMALE WORKED SLAUGHTERING CATTLE EXPOSED TO
BRAIN AND SPINAL CORD MATTER
Monday, March 29, 2010
Irma Linda Andablo CJD Victim, she died at 38 years old on February 6, 2010
in Mesquite Texas
CJD TEXAS 38 YEAR OLD FEMALE WORKED SLAUGHTERING CATTLE EXPOSED TO BRAIN
AND SPINAL CORD MATTER
Thursday, May 27, 2010
CDC - INQUIRY ABOUT vCJD DEATH OF SLAUGHTER HOUSE WORKER IRMA LINDA ANDABLO
Archive Number 20100405.1091 Published Date 05-APR-2010
Subject PRO/AH/EDR> Prion disease update 1010 (04)
snip...
[Terry S. Singeltary Sr. has added the following comment:
"According to the World Health Organisation, the future public health
threat of vCJD in the UK and Europe and potentially the rest of the world is of
concern and currently unquantifiable. However, the possibility of a significant
and geographically diverse vCJD epidemic occurring over the next few decades
cannot be dismissed.
Friday, October 23, 2009
2000-2008 Creutzfeldt-Jakob 23 Data Disease for Friday October Reporting
Surveillance Texas Years
Sunday December 16 2007
Creutzfeldt-Jakob Disease Surveillance in Texas 2000-2006
2011 Monday, September 26, 2011
L-BSE BASE prion and atypical sporadic CJD
Wednesday, March 28, 2012
VARIABLY PROTEASE-SENSITVE PRIONOPATHY IS TRANSMISSIBLE, price of prion
poker goes up again $
*** The discovery of previously unrecognized prion diseases in both humans
and animals (i.e., Nor98 in small ruminants) demonstrates that the range of
prion diseases might be wider than expected and raises crucial questions about
the epidemiology and strain properties of these new forms. We are investigating
this latter issue by molecular and biological comparison of VPSPr, GSS and
Nor98.
Tuesday, June 26, 2012
Creutzfeldt Jakob Disease Human TSE report update North America, Canada,
Mexico, and USDA PRION UNIT as of May 18, 2012
type determination pending Creutzfeldt Jakob Disease (tdpCJD), is on the
rise in Canada and the USA
Monday, July 23, 2012
The National Prion Disease Pathology Surveillance Center July 2012
Monday, August 06, 2012
Atypical neuropathological sCJD-MM phenotype with abundant white matter
Kuru-type plaques sparing the cerebellar cortex
Saturday, October 6, 2012
TRANSMISSION, DIFFERENTIATION, AND PATHOBIOLOGY OF TRANSMISSIBLE SPONGIFORM
ENCEPHALOPATHIES 2011 Annual Report
Tuesday, November 6, 2012
Transmission of New Bovine Prion to Mice, Atypical Scrapie, BSE, and
Sporadic CJD, November-December 2012 update
National Prion Disease Pathology Surveillance Center
Cases Examined1
(August 14, 2012)
see full text ;
Tuesday, November 6, 2012
Transmission of New Bovine Prion to Mice, Atypical Scrapie, BSE, and
Sporadic CJD, November-December 2012 update
older cjd reports here ;
Monday, February 13, 2012
Creutzfeldt Jakob Disease Report update USA and TEXAS Sunday, February 12,
2012
National Prion Disease Pathology Surveillance Center Cases Examined1
(August 19, 2011) including Texas
Sunday, December 2, 2012
CANADA 19 cases of mad cow disease SCENARIO 4: ‘WE HAD OUR CHANCE AND WE
BLEW IT’
Friday, December 14, 2012
Susceptibility Chronic Wasting Disease (CWD) in wild cervids to Humans 2005
- December 14, 2012
Wednesday, February 16, 2011
IN CONFIDENCE
SCRAPIE TRANSMISSION TO CHIMPANZEES
IN CONFIDENCE
why do we not want to do TSE transmission studies on chimpanzees $
snip...
5. A positive result from a chimpanzee challenged severly would likely
create alarm in some circles even if the result could not be interpreted for
man. I have a view that all these agents could be transmitted provided a large
enough dose by appropriate routes was given and the animals kept long enough.
Until the mechanisms of the species barrier are more clearly understood it might
be best to retain that hypothesis.
snip...
R. BRADLEY
Friday, February 11, 2011
Atypical/Nor98 Scrapie Infectivity in Sheep Peripheral Tissues
Monday, April 25, 2011
Experimental Oral Transmission of Atypical Scrapie to Sheep
Volume 17, Number 5-May 2011
Sunday, April 18, 2010
SCRAPIE AND ATYPICAL SCRAPIE TRANSMISSION STUDIES A REVIEW 2010
Thursday, December 20, 2012
OIE GROUP RECOMMENDS THAT SCRAPE PRION DISEASE BE DELISTED AND SAME OLD BSe
WITH BOVINE MAD COW DISEASE
Monday, August 20, 2012
CASE REPORTS CREUTZFELDT-JAKOB DISEASE: AN UNDER-RECOGNIZED CAUSE OF
DEMENTIA
see the Duke, Pa, Yale, and Mexican study here, showing the misdiagnosis of
CJD TSE prion disease as Alzheimers ;
Wednesday, May 16, 2012
Alzheimer’s disease and Transmissible Spongiform Encephalopathy prion
disease, Iatrogenic, what if ?
Proposal ID: 29403
RIP MOM 12/14/97 confirmed hvCJD...TSS December 25, 2012