Refractory nonconvulsive status epilepticus in Creutzfeldt-Jakob disease

Refractory nonconvulsive status epilepticus in Creutzfeldt-Jakob disease

Epileptic Disorders. Volume 1, Number 1, February 2009, Clinical commentary with video sequences


Author(s) : Maria Aiguabella, Mercè Falip, Misericordia Veciana, Jordi Bruna, Antoni Palasí, Luisa Corral, Jose-Ignacio Herrero, Susana Boluda, Jaume Mora, Alex Iranzo, Carme Serrano

Summary :


Creutzfeldt-Jakob disease (CJD) is a rare human transmissible spongiform subacute encephalopathy. The most common clinical manifestations of CJD include rapidly progressive dementia, behavioural changes, cerebellar dysfunction and myoclonus. Other seizure types are rare and nonconvulsive status epilepticus (SE) is exceptional. We report a case of a 44-year-old man who presented a psychotic episode followed by akinetic mutism and refractory nonconvulsive SE. The final diagnosis was CJD. Continuous video-EEG monitoring revealed the ictal pattern of nonconvulsive SE to be periodic sharp wave complexes characteristic of CJD. [Published with video sequences]

Keywords : electroencephalography, status epilepticus, nonconvulsive, Creutzfeldt-Jakob disease

http://www.john-libbey-eurotext.fr/en/revues/medecine/epd/e-docs/00/04/5B/17/resume.phtml



Thursday, May 06, 2010

Sporadic Creutzfeldt-Jakob disease mimicking nonconvulsive status epilepticus

http://creutzfeldt-jakob-disease.blogspot.com/2010/05/sporadic-creutzfeldt-jakob-disease.html



Wednesday, June 16, 2010

Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties

http://creutzfeldt-jakob-disease.blogspot.com/2010/06/defining-sporadic-creutzfeldt-jakob.html



Thursday, November 19, 2009

A case of Creutzfeldt-Jakob disease with stroke-like episode as an initial symptom

http://creutzfeldt-jakob-disease.blogspot.com/2009/11/case-of-creutzfeldt-jakob-disease-with.html



Thursday, November 05, 2009

Incidence and spectrum of sporadic Creutzfeldt–Jakob disease variants with mixed phenotype and co-occurrence of PrPSc types: an updated classification


http://creutzfeldt-jakob-disease.blogspot.com/2009/11/incidence-and-spectrum-of-sporadic.html



Saturday, April 04, 2009

An unusually presenting case of sCJD—The VV1 subtype

http://creutzfeldt-jakob-disease.blogspot.com/2009/04/unusually-presenting-case-of-scjdthe.html



Wednesday, February 04, 2009

Creutzfeldt-Jacob disease presenting as severe depression: a case report

http://creutzfeldt-jakob-disease.blogspot.com/2009/02/creutzfeldt-jacob-disease-presenting-as.html




Monday, August 03, 2009

Movement disorders reveal Creutzfeldt–Jakob disease


http://creutzfeldt-jakob-disease.blogspot.com/2009/08/movement-disorders-reveal.html




TSS