Refractory nonconvulsive status epilepticus in Creutzfeldt-Jakob disease
Epileptic Disorders. Volume 1, Number 1, February 2009, Clinical commentary with video sequences
Author(s) : Maria Aiguabella, Mercè Falip, Misericordia Veciana, Jordi Bruna, Antoni Palasí, Luisa Corral, Jose-Ignacio Herrero, Susana Boluda, Jaume Mora, Alex Iranzo, Carme Serrano
Summary :
Creutzfeldt-Jakob disease (CJD) is a rare human transmissible spongiform subacute encephalopathy. The most common clinical manifestations of CJD include rapidly progressive dementia, behavioural changes, cerebellar dysfunction and myoclonus. Other seizure types are rare and nonconvulsive status epilepticus (SE) is exceptional. We report a case of a 44-year-old man who presented a psychotic episode followed by akinetic mutism and refractory nonconvulsive SE. The final diagnosis was CJD. Continuous video-EEG monitoring revealed the ictal pattern of nonconvulsive SE to be periodic sharp wave complexes characteristic of CJD. [Published with video sequences]
Keywords : electroencephalography, status epilepticus, nonconvulsive, Creutzfeldt-Jakob disease
http://www.john-libbey-eurotext.fr/en/revues/medecine/epd/e-docs/00/04/5B/17/resume.phtml
Thursday, May 06, 2010
Sporadic Creutzfeldt-Jakob disease mimicking nonconvulsive status epilepticus
http://creutzfeldt-jakob-disease.blogspot.com/2010/05/sporadic-creutzfeldt-jakob-disease.html
Wednesday, June 16, 2010
Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties
http://creutzfeldt-jakob-disease.blogspot.com/2010/06/defining-sporadic-creutzfeldt-jakob.html
Thursday, November 19, 2009
A case of Creutzfeldt-Jakob disease with stroke-like episode as an initial symptom
http://creutzfeldt-jakob-disease.blogspot.com/2009/11/case-of-creutzfeldt-jakob-disease-with.html
Thursday, November 05, 2009
Incidence and spectrum of sporadic Creutzfeldt–Jakob disease variants with mixed phenotype and co-occurrence of PrPSc types: an updated classification
http://creutzfeldt-jakob-disease.blogspot.com/2009/11/incidence-and-spectrum-of-sporadic.html
Saturday, April 04, 2009
An unusually presenting case of sCJD—The VV1 subtype
http://creutzfeldt-jakob-disease.blogspot.com/2009/04/unusually-presenting-case-of-scjdthe.html
Wednesday, February 04, 2009
Creutzfeldt-Jacob disease presenting as severe depression: a case report
http://creutzfeldt-jakob-disease.blogspot.com/2009/02/creutzfeldt-jacob-disease-presenting-as.html
Monday, August 03, 2009
Movement disorders reveal Creutzfeldt–Jakob disease
http://creutzfeldt-jakob-disease.blogspot.com/2009/08/movement-disorders-reveal.html
TSS